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首頁 > 抗體 > 一抗 > 其它 > Glycogen Synthase 1 Monoclonal Antibody
Glycogen Synthase 1 Monoclonal Antibody
商品貨號: PLA004834
適 應(yīng) 性:
WB ELISA FCM
¥600元
規(guī)格:
在線咨詢
MSDS
說明書
商品描述
  • 發(fā)貨日期: 7
  • 基因名稱: GYS1
  • 蛋白名稱: Glycogen [starch] synthase muscle
  • Human_gene_id: 2997
  • Human_gene_link: http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=2997
  • Human_swiss_prot_no: P13807
  • Human_swiss_link: http://www.uniprot.org/uniprotkb/P13807/entry
  • Mouse_swiss_prot_no: Q9Z1E4
  • Mouse_swiss_link: http://www.uniprot.org/uniprot/Q9Z1E4
  • 特異性: Glycogen Synthase 1 Monoclonal Antibody detects endogenous levels of Glycogen Synthase 1 protein.
  • 組成: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來源: Monoclonal, Mouse
  • 稀釋: WB 1:500 - 1:2000. Flow cytometry: 1:200 - 1:400. ELISA: 1:10000. Not yet tested in other applications.
  • 純化工藝: Affinity purification
  • 儲存: -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說明書: 1
  • Msds: MSDS_Antibody.pdf
  • 其他名稱: GYS1; GYS; Glycogen [starch] synthase; muscle
  • 信號通路: Starch and sucrose metabolism;Insulin_Receptor;
  • 功能: catalytic activity:UDP-glucose ((1->4)-alpha-D-glucosyl)(n) = UDP + ((1->4)-alpha-D-glucosyl)(n+1).,disease:Defects in GYS1 are the cause of muscle glycogen storage disease type 0 (GSD0b) [MIM:611556]; also called muscle glycogen synthase deficiency. GSD0 is a metabolic disorder characterized by fasting hypoglycemia presenting in infancy or early childhood. The role of muscle glycogen is to provide critical energy during bursts of activity and sustained muscle work.,enzyme regulation:Allosteric activation by glucose-6-phosphate. Phosphorylation reduces the activity towards UDP-glucose. When in the non-phosphorylated state, glycogen synthase does not require glucose-6-phosphate as an allosteric activator; when phosphorylated it does.,function:Transfers the glycosyl residue from UDP-Glc to the non-reducing end of alpha-1,4-glucan.,pathway:Glycan biosynthesis; glycogen biosynthesis.,similarity:Belongs to the glycosyltransferase 3 family.,
  • 相關(guān)產(chǎn)品: RS0001,RS0002,YM3028,YM3029
  • 細胞定位: cytosol,membrane,inclusion body,
  • 組織表達: Endometrium,Heart,Kidney,Lymph,Muscle,Skin,
  • 科研貨號: PLA004834
Glycogen Synthase 1 Monoclonal Antibody
Catalog No PLA004834
Product information
  • 發(fā)貨日期: 7
  • 基因名稱: GYS1
  • 蛋白名稱: Glycogen [starch] synthase muscle
  • Human_gene_id: 2997
  • Human_gene_link: http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=2997
  • Human_swiss_prot_no: P13807
  • Human_swiss_link: http://www.uniprot.org/uniprotkb/P13807/entry
  • Mouse_swiss_prot_no: Q9Z1E4
  • Mouse_swiss_link: http://www.uniprot.org/uniprot/Q9Z1E4
  • 特異性: Glycogen Synthase 1 Monoclonal Antibody detects endogenous levels of Glycogen Synthase 1 protein.
  • 組成: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來源: Monoclonal, Mouse
  • 稀釋: WB 1:500 - 1:2000. Flow cytometry: 1:200 - 1:400. ELISA: 1:10000. Not yet tested in other applications.
  • 純化工藝: Affinity purification
  • 儲存: -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說明書: 1
  • Msds: MSDS_Antibody.pdf
  • 其他名稱: GYS1; GYS; Glycogen [starch] synthase; muscle
  • 信號通路: Starch and sucrose metabolism;Insulin_Receptor;
  • 功能: catalytic activity:UDP-glucose ((1->4)-alpha-D-glucosyl)(n) = UDP + ((1->4)-alpha-D-glucosyl)(n+1).,disease:Defects in GYS1 are the cause of muscle glycogen storage disease type 0 (GSD0b) [MIM:611556]; also called muscle glycogen synthase deficiency. GSD0 is a metabolic disorder characterized by fasting hypoglycemia presenting in infancy or early childhood. The role of muscle glycogen is to provide critical energy during bursts of activity and sustained muscle work.,enzyme regulation:Allosteric activation by glucose-6-phosphate. Phosphorylation reduces the activity towards UDP-glucose. When in the non-phosphorylated state, glycogen synthase does not require glucose-6-phosphate as an allosteric activator; when phosphorylated it does.,function:Transfers the glycosyl residue from UDP-Glc to the non-reducing end of alpha-1,4-glucan.,pathway:Glycan biosynthesis; glycogen biosynthesis.,similarity:Belongs to the glycosyltransferase 3 family.,
  • 相關(guān)產(chǎn)品: RS0001,RS0002,YM3028,YM3029
  • 細胞定位: cytosol,membrane,inclusion body,
  • 組織表達: Endometrium,Heart,Kidney,Lymph,Muscle,Skin,
  • 科研貨號: PLA004834
  • Hunan UPT Biotechnology Co.,Ltd
    Website:m.jx3dscan.com Servive hotline :4006916686
    E-mail:service@uptbio.com
    Address:
    Room 402, Building 13, Xinggong International Industrial Park, 100 Guyuan Road, Yuelu District, Changsha City, Hunan Province, China.
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