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首頁 > 抗體 > 一抗 > 其它 > HPS-1 Monoclonal Antibody
HPS-1 Monoclonal Antibody
商品貨號: PLA004852
適 應(yīng) 性:
WB ELISA
¥600元
規(guī)格:
在線咨詢
MSDS
說明書
商品描述
  • 發(fā)貨日期: 7
  • 基因名稱: HPS1
  • 蛋白名稱: Hermansky-Pudlak syndrome 1 protein
  • Human_gene_id: 3257
  • Human_gene_link: http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=3257
  • Human_swiss_prot_no: Q92902
  • Human_swiss_link: http://www.uniprot.org/uniprotkb/Q92902/entry
  • Mouse_swiss_prot_no: O08983
  • Mouse_swiss_link: http://www.uniprot.org/uniprot/O08983
  • 特異性: HPS-1 Monoclonal Antibody detects endogenous levels of HPS-1 protein.
  • 組成: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來源: Monoclonal, Mouse
  • 稀釋: WB 1:500 - 1:2000. ELISA: 1:10000. Not yet tested in other applications.
  • 純化工藝: Affinity purification
  • 儲存: -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說明書: 1
  • Msds: MSDS_Antibody.pdf
  • 其他名稱: HPS1; HPS; Hermansky-Pudlak syndrome 1 protein
  • 功能: alternative products:Additional isoforms seem to exist,disease:Defects in HPS1 are the cause of Hermansky-Pudlak syndrome type 1 (HPS1) [MIM:203300]. Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.,function:Component of multiple cytoplasmic organelles. Apparently crucial for their normal development and function. May be involved in intracellular protein sorting.,online information:HPS1 mutations,online information:Retina International's Scientific Newsletter,tissue specificity:Ubiquitous.,
  • 相關(guān)產(chǎn)品: RS0001,RS0002,YM3028,YM3029
  • 細胞定位: cytoplasm,lysosome,integral component of plasma membrane,cytoplasmic, membrane-bounded vesicle,BLOC-3 complex,cytoplasmic vesicle,
  • 組織表達: Ubiquitous.
  • 科研貨號: PLA004852
HPS-1 Monoclonal Antibody
Catalog No PLA004852
Product information
  • 發(fā)貨日期: 7
  • 基因名稱: HPS1
  • 蛋白名稱: Hermansky-Pudlak syndrome 1 protein
  • Human_gene_id: 3257
  • Human_gene_link: http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=3257
  • Human_swiss_prot_no: Q92902
  • Human_swiss_link: http://www.uniprot.org/uniprotkb/Q92902/entry
  • Mouse_swiss_prot_no: O08983
  • Mouse_swiss_link: http://www.uniprot.org/uniprot/O08983
  • 特異性: HPS-1 Monoclonal Antibody detects endogenous levels of HPS-1 protein.
  • 組成: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來源: Monoclonal, Mouse
  • 稀釋: WB 1:500 - 1:2000. ELISA: 1:10000. Not yet tested in other applications.
  • 純化工藝: Affinity purification
  • 儲存: -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說明書: 1
  • Msds: MSDS_Antibody.pdf
  • 其他名稱: HPS1; HPS; Hermansky-Pudlak syndrome 1 protein
  • 功能: alternative products:Additional isoforms seem to exist,disease:Defects in HPS1 are the cause of Hermansky-Pudlak syndrome type 1 (HPS1) [MIM:203300]. Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.,function:Component of multiple cytoplasmic organelles. Apparently crucial for their normal development and function. May be involved in intracellular protein sorting.,online information:HPS1 mutations,online information:Retina International's Scientific Newsletter,tissue specificity:Ubiquitous.,
  • 相關(guān)產(chǎn)品: RS0001,RS0002,YM3028,YM3029
  • 細胞定位: cytoplasm,lysosome,integral component of plasma membrane,cytoplasmic, membrane-bounded vesicle,BLOC-3 complex,cytoplasmic vesicle,
  • 組織表達: Ubiquitous.
  • 科研貨號: PLA004852
  • Hunan UPT Biotechnology Co.,Ltd
    Website:m.jx3dscan.com Servive hotline :4006916686
    E-mail:service@uptbio.com
    Address:
    Room 402, Building 13, Xinggong International Industrial Park, 100 Guyuan Road, Yuelu District, Changsha City, Hunan Province, China.
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